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KMID : 0361019860290060912
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Korean Journal of Otolaryngology - Head and Neck Surgery
1986 Volume.29 No. 6 p.912 ~ p.922
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Wegener´s Granulomatosis
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맹해성/Maeng, Hae Sung
신일식/김민식/원권희/조승호/Shin, Il Shik/Kim, Min Sik/Won, Kwon Hee/Cho, Seung Ho
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Abstract
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Wegener´s granulomatosis is an rare disease of unknown etiology but generally considered a hypersensitivity disorder.
This disease was first described by Klinger in 1931 and noted as a distinct clinicopathological syndrome by Wegener in 1936, as rhinogenic granulomatosis ; necrotizing granuloma of upper or lower respiratory tract, generalized focal necrotizing angitis and a focal necrotizing glomerulitis.
This disease is classified based on anatomic site of involvement ; classic form of Wegener´s granulomatosis and limited from of Wegener´s granulomatosis which is absent of renal invovement.
The treatment of choice is cyclophosphamide therapy with or without cortico￢steroid in this disease.
The authors, recently, have observed 1 case of classic form and 3 cases of limited form of Wegener´s granulomatosis and report these with literature review.
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KEYWORD
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